[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"health-study-detail:100589368":3},{"organization":4,"armGroups":7,"interventions":14,"overallOfficials":20,"centralContacts":27,"locations":33,"responsibleParty":59,"collaborators":61,"id":68,"slug":69,"hasResults":70,"nctId":71,"briefTitle":72,"officialTitle":73,"acronym":11,"eligibilityCriteria":74,"healthyVolunteers":70,"sex":75,"minAge":76,"maxAge":11,"enrollmentInfo":77,"targetDuration":11,"studyType":80,"phases":81,"briefSummary":83,"conditions":84,"keywords":11,"overallStatus":36,"whyStopped":11,"lastUpdateSubmitDate":89,"lastUpdatePostDateStruct":90,"startDateStruct":93,"completionDateStruct":95,"leadSponsor":97,"locationsCount":98},{"fullName":5,"class":6},"Sequitur Health Corp.","INDUSTRY",[8],{"label":9,"type":10,"description":11,"interventionNames":12},"Ammonia Device","EXPERIMENTAL",null,[13],"Diagnostic Test: Ammonia Study Device",[15],{"type":16,"name":17,"description":18,"armGroupLabels":19,"otherNames":11},"DIAGNOSTIC_TEST","Ammonia Study Device","Ammonia study device for capillary ammonia measurement",[9],[21,24],{"name":22,"affiliation":5,"role":23},"Marylaura L Thomas, Ph.D.","PRINCIPAL_INVESTIGATOR",{"name":25,"affiliation":5,"role":26},"Leslie F. Thomas, M.D.","STUDY_DIRECTOR",[28],{"name":29,"role":30,"phone":31,"phoneExt":11,"email":32},"Marylaura Thomas, Ph.D.","CONTACT","1-855-445-3889","info@sequiturhealth.com",[34],{"facility":35,"status":36,"city":37,"state":38,"zip":39,"country":40,"countryCode":41,"cosmosGeoPoint":42,"geoPoint":47,"contacts":48},"Oregon Health & Science University","RECRUITING","Portland","Oregon","97239-3098","United States","US",{"type":43,"coordinates":44},"Point",[45,46],-122.67621,45.52345,{"lat":46,"lon":45},[49,52,54,57],{"name":50,"role":30,"phone":51,"phoneExt":11,"email":11},"Amy C. Yang, M.D.","503-494-8307",{"name":53,"role":23,"phone":11,"phoneExt":11,"email":11},"Amy C Yang, M.D.",{"name":55,"role":56,"phone":11,"phoneExt":11,"email":11},"Brian Scottoline, M.D., Ph.D","SUB_INVESTIGATOR",{"name":58,"role":56,"phone":11,"phoneExt":11,"email":11},"Kimberly Kripps, M.D.",{"type":60,"investigatorFullName":11,"investigatorTitle":11,"investigatorAffiliation":11,"oldNameTitle":11,"oldOrganization":11},"SPONSOR",[62,65],{"name":63,"class":64},"Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD)","NIH",{"name":66,"class":67},"Oregon Health and Science University","OTHER","100589368","at-home-ammonia-monitoring-of-inborn-errors-of-ammonia-metabolism-100589368",false,"NCT06953505","At Home Ammonia Monitoring of Inborn Errors of Ammonia Metabolism","Pilot Study of At Home Ammonia Monitoring in Patients With an Inborn Error of Ammonia Metabolism","Inclusion Criteria:\n\n* Confirmed ammonia disorder such as\n\n  * Ornithine transcarbamylase deficiency\n  * Systemic primary carnitine deficiency\n  * Type I citrullinemia\n  * Argininosuccinic aciduria\n  * Isolated methylmalonic acidemia\n  * Type II citrullinemia\n  * Propionic acidemia\n  * Isovaleric acidemia\n  * Multiple acyl-CoA dehydrogenase deficiency\n  * Pyruvate carboxylase deficiency\n  * Argininemia (arginase deficiency)\n  * Carbamoyl phosphate synthase I deficiency\n  * Dihydrolipoamide dehydrogenase deficiency\n  * Lysinuric protein intolerance\n  * Hyperornithinemia-hyperammonemia-homocitrullinuria\n  * Carnitine-acylcarnitine translocase deficiency\n  * Carbonic anhydrase VA deficiency\n  * N-acetyl glutamate synthetase deficiency\n* English Literacy\n\nExclusion Criteria:\n\n* Incarcerated\n* Presence of a non-inborn error of metabolism medical condition associated with abnormal ammonia metabolism (e.g., end stage liver disease).\n* Unable to read in English","ALL","12 Years",{"count":78,"type":79},30,"ESTIMATED","INTERVENTIONAL",[82],"NA","The goal of this observational study is to learn if people with certain ammonia metabolism disorders will measure their ammonia levels at home.\n\nThe main question it aims to answer is:\n\n• Will participants measure their ammonia every day?\n\nParticipants will be asked to:\n\n* Attend two in-person study visits at the clinic.\n* Measure temperature, heart rate, and blood oxygen every day.\n* Complete a short survey every day.\n* Measure ammonia every day.",[85,86,87,88],"Urea Cycle Disorders","Organic Acidemias","Fatty Acid Oxidation Disorder","Ammonia; Metabolic Disorder","2026-05-21",{"date":91,"type":92},"2026-05-27","ACTUAL",{"date":94,"type":92},"2025-09-23",{"date":96,"type":79},"2027-08",{"name":5,"class":6},1]