[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"health-studies-list:{\"overallStatus\":[\"RECRUITING\",\"AVAILABLE\",\"NOT_YET_RECRUITING\"],\"leadSponsorName\":\"Sequitur Health Corp.\",\"orderBy\":\"LastUpdateSubmitDate:desc\",\"size\":25,\"offset\":0}":3,"health-study-condition:":42},{"pageToken":4,"total":5,"offset":6,"count":5,"results":7},null,1,0,[8],{"id":9,"slug":10,"hasResults":11,"nctId":12,"briefTitle":13,"officialTitle":14,"acronym":4,"eligibilityCriteria":15,"healthyVolunteers":11,"sex":16,"minAge":17,"maxAge":4,"enrollmentInfo":18,"targetDuration":4,"studyType":21,"phases":22,"briefSummary":24,"conditions":25,"keywords":4,"overallStatus":30,"whyStopped":4,"lastUpdateSubmitDate":31,"lastUpdatePostDateStruct":32,"startDateStruct":35,"completionDateStruct":37,"leadSponsor":39,"locationsCount":5},"100589368","at-home-ammonia-monitoring-of-inborn-errors-of-ammonia-metabolism-100589368",false,"NCT06953505","At Home Ammonia Monitoring of Inborn Errors of Ammonia Metabolism","Pilot Study of At Home Ammonia Monitoring in Patients With an Inborn Error of Ammonia Metabolism","Inclusion Criteria:\n\n* Confirmed ammonia disorder such as\n\n  * Ornithine transcarbamylase deficiency\n  * Systemic primary carnitine deficiency\n  * Type I citrullinemia\n  * Argininosuccinic aciduria\n  * Isolated methylmalonic acidemia\n  * Type II citrullinemia\n  * Propionic acidemia\n  * Isovaleric acidemia\n  * Multiple acyl-CoA dehydrogenase deficiency\n  * Pyruvate carboxylase deficiency\n  * Argininemia (arginase deficiency)\n  * Carbamoyl phosphate synthase I deficiency\n  * Dihydrolipoamide dehydrogenase deficiency\n  * Lysinuric protein intolerance\n  * Hyperornithinemia-hyperammonemia-homocitrullinuria\n  * Carnitine-acylcarnitine translocase deficiency\n  * Carbonic anhydrase VA deficiency\n  * N-acetyl glutamate synthetase deficiency\n* English Literacy\n\nExclusion Criteria:\n\n* Incarcerated\n* Presence of a non-inborn error of metabolism medical condition associated with abnormal ammonia metabolism (e.g., end stage liver disease).\n* Unable to read in English","ALL","12 Years",{"count":19,"type":20},30,"ESTIMATED","INTERVENTIONAL",[23],"NA","The goal of this observational study is to learn if people with certain ammonia metabolism disorders will measure their ammonia levels at home.\n\nThe main question it aims to answer is:\n\n• Will participants measure their ammonia every day?\n\nParticipants will be asked to:\n\n* Attend two in-person study visits at the clinic.\n* Measure temperature, heart rate, and blood oxygen every day.\n* Complete a short survey every day.\n* Measure ammonia every day.",[26,27,28,29],"Urea Cycle Disorders","Organic Acidemias","Fatty Acid Oxidation Disorder","Ammonia; Metabolic Disorder","RECRUITING","2026-05-21",{"date":33,"type":34},"2026-05-27","ACTUAL",{"date":36,"type":34},"2025-09-23",{"date":38,"type":20},"2027-08",{"name":40,"class":41},"Sequitur Health Corp.","INDUSTRY",""]